• 1 杭州市第一人民醫(yī)院呼吸科( 浙江杭州 310006);;
  • 2 杭州市第一人民醫(yī)院病理科( 浙江杭州 310006);

病歷摘要 患者男性,65 歲。因發(fā)熱伴咳嗽、氣短8 d就診?；肌案哐獕翰　? 年, 平素口服降壓藥, 血壓控制良好。入院體檢: 體溫38. 4 ℃, 呼吸22 次/min, 脈搏102 次/min,
血壓109 /72 mm Hg( 1 mm Hg =0. 133 kPa) , 口唇無(wú)發(fā)紺, 淺表淋巴結(jié)無(wú)腫大。頸靜脈無(wú)怒張, 左下肺叩診濁音, 余肺叩清音; 兩肺呼吸音粗, 左下肺呼吸音減弱, 可聞及少量濕啰
音。心界向左擴(kuò)大, 胸骨左緣第3 肋間可及全收縮期隆隆樣雜音3/6 級(jí), 無(wú)心包摩擦音。腹平軟, 無(wú)壓痛, 未及包塊, 肝脾肋下未及。雙下肢無(wú)腫脹。

引用本文： 沈凌,嚴(yán)秀娟,徐如君,任振義. 原發(fā)性肺動(dòng)脈肉瘤一例. 中國(guó)呼吸與危重監(jiān)護(hù)雜志, 2010, 9(5): 542-544. doi: 復(fù)制

1. Levy E, Korach A, Amir G, et al. Undifferentiated sarcoma of the pulmonary artery mimicking pulmonary thromboembolic disease.Heart Lung Circ, 2006; 15 : 62-63.
2. Chappell T, Creech CB, Parra D, et al. Presentation of pulmonary artery intimal sarcoma in an infant with a history of neonatal valvular pulmonic stenosis. Ann Thorac Surg, 2008, 85: 1092 -1094 .
3. 韓力, 時(shí)國(guó)朝, 朱雪梅, 等. 原發(fā)性肺動(dòng)脈腫瘤一例. 中國(guó)呼吸與危重監(jiān)護(hù)雜志, 2005, 4: 475 -477.
4. Bressler EL, Nelson JM. Primary pulmonary artery sarcoma:diagnosis with CT, MR imaging, and transthoracic needle biopsy.Am J Roentgenol, 1992 , 159: 702-704.
5. Winchester PA, Khilnani NM, Trost DW, et al. Endovascular catheter biopsy of a pulmonary artery sarcoma. Am J Roentgenol,1996, 167 : 657 -659.
6. Terra RM, Fernandez A, Bammann RH, et al. Pulmonary artery sarcoma mimicking a pulmonary artery aneurysm. Ann Thorac Surg,2008, 86: 1354 -1355 .
7. Nakahira A, Ogino H, Sasaki H, et al. Long-term survival of a pulmonary artery sarcoma produced by aggressive surgical resection and adjuvant chemoradiotherapy. Eur J Cardiothorac Surg, 2007 ,32: 388-390.
8. Uchida A, Tabata M, Kiura K, et al. Successful treatment of pulmonary artery sarcoma by a two-drug combination chemotherapy consisting of ifosfamide and epirubicin. Jpn J Clin Oncol, 2005, 35 :417-419.
9. Shehatha J, Saxena P, Clarke B, et al. Surgical management of extensive pulmonary artery sarcoma. Ann Thorac Surg, 2009, 87 :1269-1271.
10. Tavora F, Miettinen M, Fanburg-Smith J, et al. Pulmonary artery sarcoma: a histologic and follow-up study with emphasis on a subset of low-grade myofibroblastic sarcomas with a good long-term followup.Am J Surg Pathol, 2008, 32: 1751 -1761 .
11. Fegbeutel C, Struber M, Becker JU, et al. Recurrent sarcoma originating from the pulmonary artery 6 years after extensive thoracic resection. J Thorac Cardiovasc Surg, 2008, 136: 1093-1095.
12. Parish JM, 3rd REC, Swensen SJ, Crotty TB. Pulmonary artery sarcoma. Clinical features. Chest, 1996, 110: 1480-1488.
  1. 1. Levy E, Korach A, Amir G, et al. Undifferentiated sarcoma of the pulmonary artery mimicking pulmonary thromboembolic disease.Heart Lung Circ, 2006; 15 : 62-63.
  2. 2. Chappell T, Creech CB, Parra D, et al. Presentation of pulmonary artery intimal sarcoma in an infant with a history of neonatal valvular pulmonic stenosis. Ann Thorac Surg, 2008, 85: 1092 -1094 .
  3. 3. 韓力, 時(shí)國(guó)朝, 朱雪梅, 等. 原發(fā)性肺動(dòng)脈腫瘤一例. 中國(guó)呼吸與危重監(jiān)護(hù)雜志, 2005, 4: 475 -477.
  4. 4. Bressler EL, Nelson JM. Primary pulmonary artery sarcoma:diagnosis with CT, MR imaging, and transthoracic needle biopsy.Am J Roentgenol, 1992 , 159: 702-704.
  5. 5. Winchester PA, Khilnani NM, Trost DW, et al. Endovascular catheter biopsy of a pulmonary artery sarcoma. Am J Roentgenol,1996, 167 : 657 -659.
  6. 6. Terra RM, Fernandez A, Bammann RH, et al. Pulmonary artery sarcoma mimicking a pulmonary artery aneurysm. Ann Thorac Surg,2008, 86: 1354 -1355 .
  7. 7. Nakahira A, Ogino H, Sasaki H, et al. Long-term survival of a pulmonary artery sarcoma produced by aggressive surgical resection and adjuvant chemoradiotherapy. Eur J Cardiothorac Surg, 2007 ,32: 388-390.
  8. 8. Uchida A, Tabata M, Kiura K, et al. Successful treatment of pulmonary artery sarcoma by a two-drug combination chemotherapy consisting of ifosfamide and epirubicin. Jpn J Clin Oncol, 2005, 35 :417-419.
  9. 9. Shehatha J, Saxena P, Clarke B, et al. Surgical management of extensive pulmonary artery sarcoma. Ann Thorac Surg, 2009, 87 :1269-1271.
  10. 10. Tavora F, Miettinen M, Fanburg-Smith J, et al. Pulmonary artery sarcoma: a histologic and follow-up study with emphasis on a subset of low-grade myofibroblastic sarcomas with a good long-term followup.Am J Surg Pathol, 2008, 32: 1751 -1761 .
  11. 11. Fegbeutel C, Struber M, Becker JU, et al. Recurrent sarcoma originating from the pulmonary artery 6 years after extensive thoracic resection. J Thorac Cardiovasc Surg, 2008, 136: 1093-1095.
  12. 12. Parish JM, 3rd REC, Swensen SJ, Crotty TB. Pulmonary artery sarcoma. Clinical features. Chest, 1996, 110: 1480-1488.